Source Code Name Case count Share of cases (%)
OUTPAT OUTPAT_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica 1163
INPAT INPAT_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica 682
OUTPAT OUTPAT_ICD10(M313) Wegener's granulomatosis 537
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 437
INPAT INPAT_ICD10(M313) Wegener's granulomatosis 376
OUTPAT OUTPAT_ICD10(M316) Other giant cell arteritis 262
OUTPAT OUTPAT_ICD10(M319) Necrotizing vasculopathy, unspecified 235
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M313) Wegener's granulomatosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 191
OUTPAT OUTPAT_ICD10(M317) Microscopic polyangiitis 181
OUTPAT OUTPAT_ICD10(M311) Thrombotic microangiopathy 163
INPAT INPAT_ICD10(M319) Necrotizing vasculopathy, unspecified 142
INPAT INPAT_ICD10(M316) Other giant cell arteritis 134
OUTPAT OUTPAT_ICD10(M310) Hypersensitivity angiitis 127
OUTPAT OUTPAT_ICD10(M318) Other specified necrotizing vasculopathies 120
INPAT INPAT_ICD10(M317) Microscopic polyangiitis 115
INPAT INPAT_ICD10(M311) Thrombotic microangiopathy 102
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M316) Other giant cell arteritis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 95
INPAT INPAT_ICD10(M310) Hypersensitivity angiitis 79
INPAT INPAT_ICD10(M318) Other specified necrotizing vasculopathies 67
OUTPAT OUTPAT_ICD10(M314) Aortic arch syndrome [Takayasu] 66
INPAT INPAT_ICD9(4476A) Arteritis, unspecified 61
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M317) Microscopic polyangiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 44
INPAT INPAT_ICD10(M314) Aortic arch syndrome [Takayasu] 36
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M319) Necrotizing vasculopathy, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 35
DEATH DEATH_ICD10(M313) Wegener's granulomatosis 33
INPAT INPAT_ICD8(44698) Polyarteritis nodosa and allied conditions, Other 33
INPAT INPAT_ICD9(4462A) Hypersensitivity angiitis 28
INPAT INPAT_ICD9(4465A) Giant cell arteritis 26
INPAT INPAT_ICD9(4464A) Wegener's granulomatosis 24
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M314) Aortic arch syndrome [Takayasu]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 23
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M318) Other specified necrotizing vasculopathies. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 16
OUTPAT OUTPAT_ICD10(M312) Lethal midline granuloma 15
DEATH DEATH_ICD10(M317) Microscopic polyangiitis 14
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M310) Hypersensitivity angiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 14
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M311) Thrombotic microangiopathy. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 11
INPAT INPAT_ICD9(4467A) Takayasu's disease 9
INPAT INPAT_ICD9(4466A) Thrombotic microangiopathy 8
DEATH DEATH_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica 7
DEATH DEATH_ICD10(M319) Necrotizing vasculopathy, unspecified 6
INPAT INPAT_ICD10(M312) Lethal midline granuloma 6
INPAT INPAT_ICD8(44620) Polyarteritis nodosa and allied conditions, Other hypersensitivity angiitis 6
DEATH DEATH_ICD10(M311) Thrombotic microangiopathy 5
DEATH DEATH_ICD10(M316) Other giant cell arteritis 5